Segmental odontomaxillary dysplasia
A case report
DOI:
https://doi.org/10.61872/sdj-2026-01-02PMID:
41640379Keywords:
Entwicklungsstörung, Auftreibung Oberkiefer, Hypertrichose, Transposition ZahnkeimeAbstract
Segmental Odontomaxillary Dysplasia (SOD) is a rare, non-hereditary developmental disorder affecting one side of the maxilla, impacting hard and soft tissue as well as dentition in the affected area. The condition is often associated with enlargement of soft and hard tissue on the affected area and dental anomalies, with occasional cutaneous manifestation.
SOD is a non-progressive developmental disorder. Annual clinical and radiological follow-ups are recommended to monitor dentoalveolar development. Orthodontic treatments and dentoalveolar interventions are considered successful treatment options.
We present the case of a patient suffering from SOD and discuss the dentist’s role in early detection and the importance of the follow-up care of affected patients.
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Copyright (c) 2026 Dr. med. dent. Milica Stojicevic, Anina Baur, Caroline Airoldi-Mäder, Giulia Tochtermann, Niels Rupp, Prof. Dr. Dr. Bernd Stadlinger
This work is licensed under a Creative Commons Attribution 4.0 International License.
